Name
KARTAGENER SYNDROME
DESCRIPTION
DETAIL
TYPENOTES
Medical Care: " Antibiotics, intravenous or oral and continuous or intermittent, are used to treat upper and lower airway infections. Although prophylactic antibiotics should be used with great caution in this era of emerging antibiotic resistance, children with PCD are especially good candidates for long-term low-dose preventative antibiotics. " Obstructive lung disease, if present, should be treated with inhaled bronchodilators and aggressive pulmonary toilet. Mucolytics may be helpful. Anecdotal reports indicate that inhaled antibiotics, oral and inhaled corticosteroids, and recombinant human DNAase have been used, but no large studies support the use of these agents. Surgical Care: " Tympanostomy tubes are required to reduce conductive hearing loss and recurrent infections. o Many patients undergo repeated tympanostomy tube insertions, often complicated by chronic suppurative otitis media. o Chronic otorrhea may require special measures for aural hygiene, such as regular otomicroscopy, acetic acid irrigations, or culture-guided topical or systemic antibiotic therapy. o Because of anticipated long-term middle-ear disease, inserting tympanostomy tubes is the most sensible method of maintaining the myringotomy because the tube can be expected to stay in the tympanic membrane longer than routine grommets. " When sinus disease is refractory to medical management, functional endoscopic sinus surgery leads to transient improvement in upper and lower respiratory tract symptoms. The antiquated procedure of making a nasal antral window underneath the inferior turbinate may have a role in the management of PCD because this procedure relies on gravitational rather than ciliary clearance of mucus. Activity: Activities can be performed as tolerated; however, patients usually experience mild limitations in physical tolerance.
RELATED DISEASE
Not Available Disease
DISEASE
INVESTIGATION
X-RAY CHEST P.A. VIEW( NORMAL ), X-RAY P.N.S. ( WATERS VIEW ), ULTRA SOUND WHOLE ABDOMEN - MALE, COMPLETE BLOOD COUNT, BRONCHOSCOPY, BRONCHOGRAPHY, CT SCAN