Name
G6PD DEFICIENCY DISEASE
DESCRIPTION
DETAIL
CAUSES : - GLYCOGEN STORAGE DISEASES - SCHISTOSOMIASIS - FASCIOLIASIS - VALVULAR HEART DISEASES - HEART FAILURE - CONSTRICTIVE PERICARDITIS - VIRAL HEPATITIS A DISEASE - VIRAL HEPATITIS B DISEASE - LUPOID HEPATITIS - BUDD-CHIARI SYNDROME - VENO-OCCLUSIVE DISEASE - HAEMOLYTIC CRISIS - AMOEBIASIS - HELMINTHIC INFECTIONS - FATTY LIVER - LIVER ABCESS PYOGENIC OR AMOEBIC - AUTOIMMUNE HEPATITIS - PRIMARY BILIARY CIRRHOSIS - PRIMARY SCLEROSIG CHOLANGITIS - DRUG INDUCED LIVER DISEASE - ALCOHOLIC LIVER DISEASE - NONALCOHOLIC STEATOHEPATITIS - ALPHA-1 ANTITRYPSIN DISEASE - WILSON DISEASE - HEMOCHROMATOSIS - HEPATOCELLULAR CANCER - SECONDARIES IN LIVER - AMYLOIDOSIS - GRANULOMATOUS HEPATITIS - CRYPTOGENIC CIRRHOSISOTHER TESTS : * LIVER BIOPSY * ANTI-HEPATITIS A VIRUS IGM - FOR HEPATITIS A DISEASE * HBS AG & ANTI-HBC IGM - FOR FOR ACUTE HEPATITIS B DISEASE * HBSAG, HBEAG & / OR HBV DNA - FOR CHR HEPATITIS B DISEASE * ANTI-HCV & HCV RNA - FOR HEPATITIS C DISEASE * HBSAG & ANTI-HDV - FOR HEPATITIS D( DELTA ) DISEASE * ANTI-HEV - FOR HEPATITIS E DISEASE * ANA OR SMA , ELEVATED IGG LEVELS & COMPATIBLE HISTOLOGY - IN AUTOIMMUNE HEPATITIS * MITOCHONDRIAL ANTIBODY , ELEVATED IGM LEVELS & COMPATIBLE HISTOLOGY - PRIMARY BILIARY CIRRHOSIS * P-ANCA , CHOLENGIOGRAPHY - PRIMARY SCLEROSING CHOLANGITIS * ANTITRYPSIN LEVELS - REDUCED & PHENOTYPES PIZZ OR PISZ - ALPHA-1 ANTITRYPSIN DISEASE * ALPHA FETOPROTEIN LEVELS - INCREASED IN HEPATOCELLULAR CANCER
TYPENOTES
RELATED DISEASE
Not Available Disease
Disease
Remarks
HEPATOMEGALY
SERIAL ULTRA SOUNDS SHOULD BE DONE ROUTINELY TO MONITOR CHANGES IN HEPATIC ADENOMA IF THAT IS THE CAUSE FOR HEPATOMEGALY
DISEASE
INVESTIGATION
AUSTRALIA ANTIGEN(HBSAG), MONTOUX TEST, X-RAY CHEST P.A. VIEW( NORMAL ), ULTRA SOUND WHOLE ABDOMEN - MALE, COMPLETE BLOOD COUNT, ECHOCARDIOGRAPHY, ECG, CT SCAN ABDOMEN, LIVER FUNCTION TEST, BIOPSY