Name
DUBIN JOHNSON SYNDROME
DESCRIPTION
DETAIL
D.D. : * ROTOR SYNDROMEOTHER TESTS : * LIVER IS GROSSLY BLACK IN COLOR DUE TO ACCUMULATION OF DARK, COARSLY GRANULAR PIGMENT IN LYSOSOMES OF CENTRILOBULAR HEPATOCYTES. * PREDOMINANT RISE IN CONJUGATED BILIRUBIN * BILIRUBINURIA IS CHARACTERISTICALLY PRESENT * DIAGNOSTIC ABNORMALITY IN URINARY COPROPORPHYRIN EXCRETION. TOTAL COPROPORPHYRIN EXCRETION IS NORMAL BUT > 80% IS ISOMER I. * ON ORAL CHOLECYSTOGRAM, GALL BLADDER IS NOT VISUALISED
TYPENOTES
RELATED DISEASE
Not Available Disease
DISEASE
INVESTIGATION
URINE FOR BILE SALTS AND BILE PIGMENTS, COMPLETE BLOOD COUNT, LIVER FUNCTION TEST, BIOPSY