Name
HEPATITIS-B DISEASE, ACUTE
DESCRIPTION
DETAIL
TRIGERING FACTORS : - SUN LIGHT, ALCOHOL USE, OESTROGENS, IRON, LIVER DISEASE PARTICULARLY HEPATITIS C DISEASE* HEPATIC URO-DECARBOXYLASE IS DEFICIENT IN ALL FORMS OF DISEASE. IN TYPE I & III, URO DECARBOXYLASE ENZYME IS NORMAL IN RBC & IN TYPE II, IT IS DEFICIENT IN RBC & OTHER TISSUES. IN TYPE III, DEFICIENCY IS LIMITED TO LIVER ONLY. * SERUM & URINARY AMINOLEVULINIC ACID ( ALA ) LEVEL ARE INCREASED * PORPHOBILINOGEN ( PBG ) LEVELS - NORMAL * PORPHYRINES ARE INCREASED IN URINE , STOOL, LIVER & PLASMA
TYPENOTES
CAN BE SPORADIC.* - ATTACK TRIGGERING FACTORS : SUN LIGHT, ALCOHOL, IRON, OESTROGENS, LIVER DISEASE PARTICULARLY HEPATITIS C DISEASE OTHER THAN CERTAIN DRUGS, HEXACHLOROBENZENE * - PT HAVE LIVER DAMAGE & ARE AT INCREASED RISK FOR HEPATOCELLULAR CARCINOMA. * REPEATED PHLEBOTOMY TO REDUCE HEPATIC IRON IS INDICATED. SERUM FERRITIN & HAEMOGLOBIN LEVELS SHOLD BE FOLLOWED CLOSELY TO PREVENT IRON DFICIENCY. * CHLOROQUINE OR HYDROXYCHLOROQUINE IN SMALL DOSES( 125 MG TWICE A WEEK ) .
RELATED DISEASE
Not Available Disease
Disease
Remarks
PORPHYRIA CUTANEA TARDA
ASSOCIATION CAN PRECIPITATE ATTACK OF BLISTERS
DISEASE
INVESTIGATION
COMPLETE BLOOD COUNT