Name
PORPHYRIA CUTANEA TARDA
DESCRIPTION
DETAIL
POSSIBLE ASSOCIATED DISEASES: 1. HAEMATOLOGIC COMPLICATIONS : - HAEMATOLOGIC MANIFESTATIONS OF HYPERSPLENISM - AUTOIMMUNE HAEMOLYTIC ANEMIA - COOMBS POSITIVE HAEMOLYTIC ANEMIA - PERNICIOUS ANEMIA - IDIOPATHIC THROMBOCYTOPENIC PURPURA - EOSINOPHILIA 2. GASTROINTESTINAL COMPLICATIONS : - INFLAMMATORY BOWEL DISEASE - ULCERATIVE COLITIS - CELIAC DISEASE 3. PROLIFERATIVE GLOMERULONEPHRITIS 4. FIBROSING ALVEOLITIS 5. PERICARDITIS & MYOCARDITIS 6. ENDOCRINOLOGIC MANIFESTATIONS : - GRAVES DISEASE - AUTOIMMUNE THYROIDITIS - JUVENILE DIABETES MELLITUS 7. RHEUMATOLOGIC COMPLICATIONS : - RHEUMATOID ARTHRITIS - FELTY SYNDROME - SJOGREN SYNDROME - SYSTEMIC SCLEROSIS - MIXED CONNECTIVE TISSUE DISEASE - ERYTHEMA NODOSUM - LEUKOCYTOCLASTIC VASCULITIS 8. FEBRILE PANNICULITIS 9. LICHEN PLANUS 10. UVEITIS* IMMUNOELECTROPHORESIS - IGG PREDOMINANT POLYCLONAL HYPERGAMMAGLOBULINEMIA IS COMMON * ANTI-LIVER-KIDNEY MICROSOMAL ANTIBODIES [ ANTI-LKM-1 ] - MAY BE POSITIVE * ANTIBODIES AGAINST SOLUBLE LIVER ANTIGEN [ ANTI-SLA ] - MAY BE POSITIVE * ANTIPHOSPHOLIPID ANTIBODIES * ANTIBODIES TO LIVER SPECIFIC ASIALOGLYCOPROTEIN RECEPTOR OR HEPATIC LECTIN * LIVER FUNCTION TESTS - ABNORMAL * S. ALK PHOSPHATASE - A SHARP INCREASE MAY REFLECT DEVELOPMENT OF PRIMARY SCLEROSING CHOLANGITIS OR ONSET OF HEPATOCELLULAR CARCINOMA * CBC - MAY BE MILD LEUKOPENIA, NORMOCHROMIC ANEMIA, COOMBS POSITIVE HEMOLYTIC ANEMIA, THROMBOCYTOPENIA, RAISED ESR, EOSINOPHELIA * LIVER BIOPSY - TO CONFIRM FINAL REMMISION OR DIAGNOSIS
TYPENOTES
A SHARP INCREASE IN S. ALK. PHOSPHATASE MAY INDICATE PRIMARY SCLEROSING CHOLANGITIS OR HEPATOCELLULAR CARCINOMA.
RELATED DISEASE
Not Available Disease
Disease
Remarks
HEPATITIS, AUTOIMMUNE
ASSOCIATION CAN PRECIPITATE ATTACK OF BLISTERS
DISEASE
INVESTIGATION
ANTI-NUCLEAR ANTIBODY TEST, ANTI-MITOCONDRIAL ANTIBODIES, LIVER FUNCTION TEST, ANTI-SMOOTH MUSCLE ANTIBODY TEST, PROTEIN ELECTROPHORESIS
[HEPATITIS, AUTOIMMUNE]