Name
HIGH HDL CHOLESTEROL ( HYPERALPHALIPOPROTEINEMIA OR HALP )
DESCRIPTION
DETAIL
CAUSES : 1. PRIMARY CAUSES DUE TO * PRIMARY HALP ( FAMILIAL ) * CETP ( CHOLESTERYL ESTER TRANSFER PROTEIN ) DEICIENCY * FAMILIAL HEPATIC LIPASE DEFICIENCY * SELECTIVE UP-REGULATION OF APO A-1 PRODUCTION * LCAT (LECITHIN-CHOLESTEROL ACETYLTRANSFERASE)OVEREXPRESSION 2. SECONDARY CAUSES : * VIGOROUS & SUSTAINED AEROBIC EXERCISES LIKE LONG DISTANCE RUNNING * REGULAR SUBSTANTIAL ALCOHOL INTAKE * TREATMENT WITH ORAL ESTROGENS * TREATMENT WITH NICOTINIC ACID AT DOSES > 1 GM/DAY * TREATMENT WITH PHENYTOIN * PRIMARY BILIARY CIRRHOSIS * TREATMENT WITH FIBRATES -------------------------------------------------------------------------- D.D. : - JUVENILE CORNEAL OPACIFICATION - MULTIPLE SYSTEMIC LIPOMATOSIS - LONGEVITY SYNDROME - ALCOHOL CONSUMPTION, HEAVY - USE OF ORAL UNOPPOSED OESTROGENS - USE OF HIGH DOSE NICOTINIC ACID - USE OF PHENYTOIN - TREATMENT WITH FIBRATES* PLASMA HDL APOLIPOPROTEINS - HIGH
TYPENOTES
Medical Care Most patients with HALP are incidentally diagnosed following blood testing. Generally, patients are asymptomatic and no medical therapy is required. " Patients with corneal opacity may need an evaluation by an ophthalmologist. " Patients in whom excessive alcohol consumption is a cause of elevated HDL-C levels should be assessed for the possible consequences of this habit. Diet Certain forms of dietary therapy, including diets low in fat content, have been shown to influence the levels of alpha-lipoproteins and HDL-C in plasma. A low-fat diet may cause some reduction in HDL-C levels, while high-fat diets are associated with higher HDL-C levels. DRUG TREATMENT : REQUIRE NO DRUG TEATMENT BECAUSE ASYMPTOMATIC PRESENTATION.
RELATED DISEASE
Not Available Disease
DISEASE
INVESTIGATION
COMPLETE BLOOD COUNT, LIPIDS PROFILE