Name
VIPOMAS
DESCRIPTION
DETAIL
IT IS A NEUROENDOCRINE TUMOR, MAINLY FOUND IN PANCRES THAT SECRETS VIP AUTONOMOUSLY. D.D. : - CARCINOID TUMOR - INTESTINAL - GASTRINOMA - GASTROENTERITIS, BACTERIAL - PANCREATIC CANCER - SOMATOSTATINOMAS - SPRUE, TROPICAL - THYROID MEDULLARY CARCINOMA - VILLOUS ADENOMA - WERMER SYNDROME - ZOLLINGER-ELLISON SYNDROME* SERUM VIP ( VASOACTIVE INTESTINAL POLYPEPTIDES- NORMAL LEVELS 20-30 PMOL/L OR LESS ) LEVELS DONE AFTER FASTING & COLLECT SERUM DURING BOUT OF DIARRHEA - RAISED * ULTRA SOUND ABDOMEN, CT ABDOMEN, CELIAC ANGIOGRAPHY, AORTOGRAPHY ARE FREQUENTLY INSENSITIVE & MAY LOCALIZE ABOUT 60% OF VIPOMAS. * ENDOSCOPIC ULTRA SOUND OR INTRAOPERATIVE ULTRA SOUND * TRANSHEPATIC PORTAL VENOUS SAMPLE MAY LOCALIZE OCCULT TUMORS. * LOCALIZATION MAY BE DONE BY MEASURING LEVELS OF VASOACTIVE INTESTINAL POLYPEPTIDES IN THE RT. HEPATIC VEIN. * SERUM POTASSIUM LEVELS - LOW * NON-ANION GAP ACIDOSIS - PRESENT * SERUM MAGNESIUM - LOW DUE TO DIARRHEA * SERUM CALCIUM LEVELS - INCREASED * CT ABDOMEN OR MRI - TO LOCATE TUMOR IN PANCREAS * SOMATOSTATIN RECEPTOR SCINTIGRAPHY * TECNITIUM 99M SESTAMIBI - FOR LOCALIZING VIPOMAS
TYPENOTES
RELATED DISEASE
Not Available Disease
DISEASE
INVESTIGATION
SERUM CALCIUM, SERUM POTASSIUM, SERUM MAGNESIUM, MRI BRAIN ( FUNCTIONAL ), COMPLETE BLOOD COUNT, CT SCAN ABDOMEN